Fetopathology and developmental pathology of the embryo and fetus: Myeloschisis (rachischisis posterior)

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+ Atlas of fetal pathology

+ Congenital malformations

+ Physiological developement of an embryo and fetus, growth and changes of the external shape

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+ Congenital malformations of individual organ systems

+ Congenital malformations of the central nervous system

+ Congenital malformations of the spinal cord

+ Spina bifida

+ Myeloschisis (rachischisis posterior)

+ Congenital malformations of the brain

+ Anencephaly

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+ Encephalocele

+ Arnold-Chiari malformation

+ Disorders of formation of the structures derived from the mediobasal prosencephalon

+ Migration disorders

+ Destructive lesions of fetal brain (disruptions)

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+ Renal agenesis

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+ Congenital malformations associated with congenital malformations of urinary system

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+ Pulmonary atresia with intact ventricular septum

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+ Oral cavity and the palate

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+ Atresia

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+ Omphalocele

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+ Pentalogy of Cantrell

+ Developemental anomalies of the skeleton

+ Defects of growth of tubular bone and/or spine

+ Thanatophoric dysplasia

+ Diastrophic dysplasia

+ Abnormalities of density of cortical diaphyseal structure or metaphyseal modeling

+ Osteogenesis imperfecta

+ Limb malformations

+ Terminal transverse limb defects

+ Radial ray defects

+ Finger anomalies

+ Club foot

+ Constriction (amniotic) band syndrome

+ Placental inflammation

+ Ascending infections

+ Placental inflammation, acute

+ Hematogenous infections

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+ Pathology of the fetal membranes

+ Amniotic band syndrome

+ Meconium staining

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+ Abnormal length

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+ Miscellaneous rare cord lesions

Myeloschisis (rachischisis posterior)

Clinical signs

severe open defect, the neural tissue is bare with no dermal or meningeal covering.
always associated with serious functional disorders of the spinal cord
the most severe form of spina bifida, affected newborns die very soon
craniorachischisis totalis is a complete neural tube defect with missing neurocranium and rachischisis.

Rhachischisis posterior (73334)

Pictures

Lumbosacral rachischisis, 22-week fetus: Rhachischisis, Macro, autopsy (72524)

Rhachischisis posterior: Rhachischisis posterior, Macro, autopsy (73333) Rhachischisis posterior, Macro, autopsy (73334) Rhachischisis posterior, Macro, autopsy (73335)

Atypical shape of the occipital region (Arnold Chiari malformation), together with lumbosacral rachischisis, 22-week fetus: Rhachischisis, Macro, autopsy (72523)

Spina bifida aperta, US video: Spina bifida aperta, Ultrasound, video (74030)