Fetopathology and developmental pathology of the embryo and fetus: Arnold-Chiari malformation

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+ Atlas of fetal pathology

+ Congenital malformations

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Arnold-Chiari malformation

Clinical signs

abnormally shaped bone structures in the posterior cranial fossa (small posterior fossa, low attachement of the tentorium cerebelli)
the inferior vermis, cerebellar tonsils and distal brain stem are displaced down through the foramen occipitale magnum into the upper cervical canal, where they are damaged due to high pressure
hydrocephalus is a rule
Arnold Chiari malformation is almost always associated with lumbosacral meningomyelocele
additional malformations of the brain, such as cerebral heterotopy, corpus callosum agenesis, abnormal gyrification can be found

Arnold-Chiariho malformation (72122)

Pictures

Arnold-Chiari malformation: Arnold-Chiari malformation, Macro, autopsy (72122) Arnold-Chiari malformation, Macro, autopsy (72123)