Fetopathology and developmental pathology of the embryo and fetus: Congenital pulmonary lymphangiectasia

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+ Atlas of fetal pathology

+ Congenital malformations

+ Physiological developement of an embryo and fetus, growth and changes of the external shape

+ Congenital malformations and congenital anomalies

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+ Etiology of congenital anomalies (CA)

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+ Sirenomelia (Mermaid syndrome)

+ Hydrops fetalis

+ Immune hydrops (erythroblastosis fetalis, hemolytic disease of the newborn)

+ Nonimmune hydrops

+ Hygroma colli cysticum

+ Pierre-Robin sequence

+ Caudal regression syndrome (sacral agenesis)

+ VACTERL association

+ Pathology of twinning

+ Complications of monochorionic diamnionic placentation

+ Chronic twin transfusion syndrome

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+ Congenital malformations in twins

+ Chorangiopagus parasiticus (acardius)

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+ Monsters

+ Monstra duplicia

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+ Congenital malformations of individual organ systems

+ Congenital malformations of the central nervous system

+ Congenital malformations of the spinal cord

+ Spina bifida

+ Myeloschisis (rachischisis posterior)

+ Congenital malformations of the brain

+ Anencephaly

+ Iniencephaly

+ Encephalocele

+ Arnold-Chiari malformation

+ Disorders of formation of the structures derived from the mediobasal prosencephalon

+ Migration disorders

+ Destructive lesions of fetal brain (disruptions)

+ Porencephaly

+ Hydranencephaly

+ Hydrocephalus

+ Dandy-Walker malformation

+ Intracranial non-neoplastic cysts

+ Arachnoid cyst

+ Neuroepithelial cyst

+ Congenital malformations of the respiratory system

+ Congenital cystic adenomatoid malformation (CCAM)

+ Lobar sequestration

+ Congenital lobar emphysema

+ Pulmonary hyperplasia

+ Pulmonary hypoplasia

+ Congenital pulmonary lymphangiectasia

+ Diaphragm and congenital malformations

+ Congenital malformations of kidneys and efferent urinary tracts

+ Renal agenesis

+ Variations of shape and position of the kidneys

+ Renal cystic disease

+ Infantile polycystic kidneys (ARKPD)

+ Renal dysplasia

+ Adult polycystic kidneys (ADPKD)

+ Autosomal dominant polycystic kidney disease in infant and fetus

+ Lower urinary tract obstruction

+ Posterior urethral valves

+ Congenital tubular renal dysgenesis

+ Urinary bladder

+ Hypospadia

+ Congenital malformations of genital system and somatosexual congenital disorders

+ Somatosexual disorders

+ Somatosexual disorders with normal karyotype

+ Pseudohermaphroditism masculinus

+ Androgen insensitivity syndrome, testicular feminization syndrome, female XY

+ Pseudohermaphroditism femininus

+ Congenital adrenal hyperplasia

+ Somatosexual disorders with pathologic karyotype

+ Congenital malformations of female genitalia

+ Congenital malformations of the internal genitalia

+ Congenital malformations associated with congenital malformations of urinary system

+ Congenital malformations of the vulva

+ Congenital malformations of the male genital organs

+ Cryptorchidism

+ Congenital malformations of penis and scrotum

+ Smith-Lemli-Opitz syndrome (SLOS)

+ Congenital tumors

+ Sacrococcygeal teratoma

+ Congenital cardiac rhabdomyoma

+ Congenital heart defects

+ Defects of heart septum

+ Atrial septal defects

+ Ventricular septal defects

+ AV septal defects

+ Anomalies of the great arteries

+ Transposition of the great arteries

+ Truncus arteriosus

+ Double-outlet right ventricle

+ Malformations of the valves

+ Tricuspid atresia

+ Stenosis and atresia of the mitral valve, the hypoplastic left heart syndrome

+ Stenosis of the pulmonary artery

+ Pulmonary atresia with intact ventricular septum

+ Tetralogy of Fallot

+ Aortic stenosis

+ Malformations of the aortic arch system

+ Persistence of ductus arteriosus

+ Coarctation of the aorta

+ Interruption of the aortic arch

+ Right-sided aortic arch

+ Malformations of the venous system

+ Anomalies of situs and heart position

+ Di George syndrome

+ Congenital malformations of the gastrointestinal tract

+ Oral cavity and the palate

+ Cleft lip and palate

+ Congenital defects of the esophagus

+ Atresia

+ Congenital esophagus stenoses

+ Congenital malformations of the stomach

+ Congenital malformations of the intestines

+ Atresia

+ Malrotation of the intestine

+ Remnants of the omphalomesentric duct

+ Anorectal malformations

+ Duplicatures

+ Defects of the abdominal wall

+ Omphalocele

+ Gastroschisis

+ Limb-body wall complex

+ Pentalogy of Cantrell

+ Developemental anomalies of the skeleton

+ Defects of growth of tubular bone and/or spine

+ Thanatophoric dysplasia

+ Diastrophic dysplasia

+ Abnormalities of density of cortical diaphyseal structure or metaphyseal modeling

+ Osteogenesis imperfecta

+ Limb malformations

+ Terminal transverse limb defects

+ Radial ray defects

+ Finger anomalies

+ Club foot

+ Constriction (amniotic) band syndrome

+ Placental inflammation

+ Ascending infections

+ Placental inflammation, acute

+ Hematogenous infections

+ Fetomaternal listeriosis

+ Pathology of the fetal membranes

+ Amniotic band syndrome

+ Meconium staining

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+ Hydatidiform mole

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+ Abnormal length

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+ Acute funisitis

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+ Miscellaneous rare cord lesions

Congenital pulmonary lymphangiectasia

Clinical signs

rare disease
the pleura rupture and chylothorax may develop
the occurence is isolated or combined with other congenital malformations, mostly heart defects

Histology

The lymfatic dilatation is sometimes cystic in pleura, subpleura and within the septa.