Fetopathology and developmental pathology of the embryo and fetus: Truncus arteriosus

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+ Atlas of fetal pathology

+ Congenital malformations

+ Physiological developement of an embryo and fetus, growth and changes of the external shape

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+ Defects of heart septum

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+ Anomalies of the great arteries

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+ Truncus arteriosus

+ Double-outlet right ventricle

+ Malformations of the valves

+ Tricuspid atresia

+ Stenosis and atresia of the mitral valve, the hypoplastic left heart syndrome

+ Stenosis of the pulmonary artery

+ Pulmonary atresia with intact ventricular septum

+ Tetralogy of Fallot

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+ Malformations of the aortic arch system

+ Persistence of ductus arteriosus

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+ Anomalies of situs and heart position

+ Di George syndrome

+ Congenital malformations of the gastrointestinal tract

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+ Terminal transverse limb defects

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+ Constriction (amniotic) band syndrome

+ Placental inflammation

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+ Miscellaneous rare cord lesions

Truncus arteriosus

Macroscopic appearance

a single arterial trunk arises from the base of the heart supplying the pulmonary, systemic and coronary arteries
the truncus overrides a large ventricular septal defect
truncal valve is tricuspid, the cusps are often thickened and dysplastic

Clinical signs

mixing of the systemic and pulmonary venous blood flow at the level of the truncus during systole
affected infants present in the first two months of life with heart failure, cyanosis is mild
truncal insufficiency is seen in 15% of the cases, its presence worsens the outcome of the surgical correction
rare defect, typical of Di George syndrome

Pictures

Truncus arteriosus communis: Truncus arteriosus communis, Macro, autopsy (71954)

Truncus arteriosus communis: Truncus arteriosus, Macro, autopsy (73226) Truncus arteriosus, Macro, autopsy (73227) Truncus arteriosus, Macro, autopsy (73228)

Truncus arteriosus communis: Truncus arteriosus communis, Macro, autopsy (73347)