Fetopathology and developmental pathology of the embryo and fetus: Porencephaly

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+ Atlas of fetal pathology

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+ Hydranencephaly

+ Hydrocephalus

+ Dandy-Walker malformation

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+ Congenital malformations of the respiratory system

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+ Pentalogy of Cantrell

+ Developemental anomalies of the skeleton

+ Defects of growth of tubular bone and/or spine

+ Thanatophoric dysplasia

+ Diastrophic dysplasia

+ Abnormalities of density of cortical diaphyseal structure or metaphyseal modeling

+ Osteogenesis imperfecta

+ Limb malformations

+ Terminal transverse limb defects

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+ Constriction (amniotic) band syndrome

+ Placental inflammation

+ Ascending infections

+ Placental inflammation, acute

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Porencephaly

Introduction

Fluid — filled cavity (pseudocyst) originating during fetal life.

Clinical signs

Clinical presentation depends on the extent and location of the defect: cerebral palsy, developemental delay, epilepsy, blindness.

Macroscopic appearance

smooth walled cavity in a hemispere
unilateral or bilateral
deep defects allow communacation between the ventricle and the surface covered only by a thin external membrane
the cortex at the edge of the cavity may show polymicrogyria
polymicrogyria is frequently seen in the contralateral hemispere in unilateral porencephaly

Porencephaly (74425)

Pictures

Porencephaly, 7-week infant: Porencephaly, Macro, autopsy (73331) Porencephaly, Macro, autopsy (73332)

Porencephaly: Porencephaly, Macro, autopsy (74424) Porencephaly, Macro, autopsy (74425) Porencephaly, Macro, autopsy (74426) Porencephaly, Macro, autopsy (74427) Porencephaly, Macro, autopsy (74428)