Fetopathology and developmental pathology of the embryo and fetus: Dandy-Walker malformation

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+ Atlas of fetal pathology

+ Congenital malformations

+ Physiological developement of an embryo and fetus, growth and changes of the external shape

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+ Terminal transverse limb defects

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+ Constriction (amniotic) band syndrome

+ Placental inflammation

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Dandy-Walker malformation

Clinical signs

Clinically it resembles the hydrocephalus. Affected persons can live up to their twenties.

Macroscopic appearance

agenesis or hypoplasia of the cerebellar vermis
cystic dilatation of the 4th ventricle
obstruction of the foramina rhombencephali
larger posterior cranial fossa
hydrocephalus
sometimes even agenesis of the corpus callosum and gyrification disorders

Dandy-Walker malformation (72361)

Dandy-Walker malformation (72362)

Pictures

Dandy-Walker malformation, agenesis of the corpus callosum, child 2 years old, hydrocephalus: Dandy Walker, hydrocephalus, Macro, autopsy (72357)

Dandy-Walker malformation, cerebellum: Dandy Walker, cerebellum, Macro, autopsy (72358) Dandy Walker, cerebellum, Macro, autopsy (72359)

Agyria, agenesis of the corpus callosum, Dandy-Walker syndrome, child 2 years old: Dandy Walker, agyria, agenesis of the corpus callossum, Macro, autopsy (72360)

Cystic dilatation of the 4th ventricle: Dandy Walker, cystic dilatation of the 4th ventricle, Macro, autopsy (72361) Dandy Walker, cystic dilatation of the 4th ventricle, Macro, autopsy (72362)