One year later she came in with relaps in the upper jaw/paranasal region and in the splanchnocranium. Furhermore, two cystic lesion in the right lung of uncertain significance were found on the high resolution CT scan.
Considering the possibility of Erdheim-Chester disease (possible lung involvement), the diagnostic slides were send to Dr. Ronald Jaffe, Children’s Hospital of Pittsburgh for second opinion. Diagnosis of relapsing Rosai-Dorfman disease was confirmed.
Our patient has started chemotherapy according to LCH III. course 1+2 + continuation treatment).
Sheets of (sometimes atypical) histiocytes in mixture with lymphocytes.
The case was closed as recurrency of Rosai-Dorfman disease.
Top of this page